지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2012.1
- 수록면
- 293 - 300 (8page)
이용수
초록· 키워드
오류제보하기
Background and Purpose Recently published, evidence-based guidelines should alter the management of amyotrophic lateral sclerosis (ALS)/motor neuron disease (MND). However, the newest recommendations for ALS/MND therapy are not reflected in actual clinical practice. We sought to evaluate the current status of the diagnosis and management of ALS in Korea.
Methods The Korean ALS/MND research group was organized in 2010, involving more than 50 neurologists from neuromuscular centers in Korea. Participating centers collected data from April to September 2010 on the diagnosis and management of patients with ALS. Data forms from the ALS patient care database, which is a component of the ALS clinical assessment, research, and education program (http://www.outcomes-umassmed.org/ALS/), were modified and used for data collection.
Results In total, 373 sporadic ALS cases from 35 centers were enrolled. The demographic features and clinical findings were similar to those in previous reports from other countries. The mean age at onset was 50-60 years, and a slight male predominance was observed. The enrolled patients predominantly showed focal onset of cervical or lumbosacral symptoms. Only about onehalf of the indicated patients (31.4%) received a physician’s recommendation for a parenteral gastrostomy, and 18.1% underwent the procedure. Noninvasive ventilation was recommended in 23%of patients, but applied in only 9.5% of them. Tracheostomy was performed in 12.7% of patients.
Conclusions The demographic and clinical features of the diagnosis and management of ALS in Korea are similar to those reported in other countries; however, supportive management, as recommended in evidence-based guidelines, are not yet widely recommended or performed for patients with ALS in Korea.
목차
등록된 정보가 없습니다.
참고문헌 (21)
참고문헌 신청
Bae JS / 2008 / A proposal for the establishment of an Korean ALS database / J Korean Neurol Assoc 26 (3) : 106 ~ 107
Beghi E / 2006 / 127th ENMC International Workshop: implementation of a European registry of ALS. Naarden, The Netherlands, 8-10 October / Neuromuscul Disord 16 : 46 ~ 53
Bradley WG / 2001 / Current management of ALS: comparison of the ALS CARE Database and the AAN Practice Parameter. The American Academy of Neurology / Neurology 57 : 500 ~ 50
Brooks BR / 1994 / El Escorial World Federation of Neurology criteria for the diagnosis of amyotrophic lateral sclerosis. Subcommittee on Motor Neuron Diseases/Amyotrophic L
Desport JC / 1999 / Nutritional status is a prognostic factor for survival in ALS patients / Neurology 53 : 1059 ~ 1063
Beghi E / 2006 / 127th ENMC International Workshop: implementation of a European registry of ALS. Naarden, The Netherlands, 8-10 October / Neuromuscul Disord 16 : 46 ~ 53
Bradley WG / 2001 / Current management of ALS: comparison of the ALS CARE Database and the AAN Practice Parameter. The American Academy of Neurology / Neurology 57 : 500 ~ 50
Brooks BR / 1994 / El Escorial World Federation of Neurology criteria for the diagnosis of amyotrophic lateral sclerosis. Subcommittee on Motor Neuron Diseases/Amyotrophic L
Desport JC / 1999 / Nutritional status is a prognostic factor for survival in ALS patients / Neurology 53 : 1059 ~ 1063
이 논문의 저자 정보
최근 본 자료
댓글(0)
0