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학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
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연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2021.6
- 수록면
- 247 - 251 (5page)
- DOI
- https://doi.org/10.3904/kjm.2021.96.3.247
이용수
초록· 키워드
오류제보하기
Hereditary hemorrhagic telangiectasia (HHT) is an uncommon autosomal dominant disorder resulting in vascular malformation, such as pulmonary arteriovenous malformation (PAVM). Here, we report a rare case of pulmonary arteriovenous malformation caused by HHT in a hemodialysis (HD) patient. A 34-year-old man receiving maintenance HD via radiocephalic arteriovenous fistula developed progressive dyspnea without definite pulmonary edema. His mother had been diagnosed with HHT. He had experienced multiple episodes of epistaxis and had been intermittently treated with blood transfusions because of severe anemia. Blood gas analysis showed hypoxia. Chest computed tomography revealed multiple dilated vessels of variable sizes, continuous with the pulmonary artery throughout both lung fields, consistent with PAVM. After treating pulmonary artery embolization at the largest PAVM, he recovered from his dyspnea symptoms and hypoxia.
목차
등록된 정보가 없습니다.
참고문헌 (9)
참고문헌 신청
Meier NM / 2018 / Hereditary hemorrhagic telangiectasia and pulmonary arteriovenous malformations : clinical aspects / Cardiovasc Diagn Ther 8:316~324
Parambil JG / 2016 / Hereditary hemorrhagic telangiectasia / Clin Chest Med 37:513~521
Begbie ME / 2003 / Hereditary haemorrhagic telangiectasia(Osler-Weber-Rendu syndrome) : a view from the 21st century / Postgrad Med J 79:18~24
Shovlin CL / 1999 / Hereditary haemorrhagic telangiectasia and pulmonary arteriovenous malformations : issues in clinical management and review of pathogenic mechanisms / Thorax 54:714~729
Navratil M / 2013 / Pulmonary arteriovenous malformations presenting as difficult-to-control asthma : a case report / J Med Case Rep 7:32
Parambil JG / 2016 / Hereditary hemorrhagic telangiectasia / Clin Chest Med 37:513~521
Begbie ME / 2003 / Hereditary haemorrhagic telangiectasia(Osler-Weber-Rendu syndrome) : a view from the 21st century / Postgrad Med J 79:18~24
Shovlin CL / 1999 / Hereditary haemorrhagic telangiectasia and pulmonary arteriovenous malformations : issues in clinical management and review of pathogenic mechanisms / Thorax 54:714~729
Navratil M / 2013 / Pulmonary arteriovenous malformations presenting as difficult-to-control asthma : a case report / J Med Case Rep 7:32
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