지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
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연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2015.1
- 수록면
- 180 - 185 (6page)
이용수
초록· 키워드
오류제보하기
Hemophagocytic lymphohistiocytosis (HLH) is a rare disorder characterized by fever, pancytopenia, hyperferritinemia, and phagocytosis of hematopoietic cells in bone marrow, liver, or lymph nodes. HLH can occur during the course of systemic lupus erythematosus (SLE), but can also be a presenting manifestation. Because development of pancytopenia occurs in less than 10 percent of SLE cases, investigation for HLH is necessary when otherwise unexplained pancytopenia persists despite adequate treatment. We experienced three cases of secondary HLH associated with SLE. Among the three patients, two patients developed HLH during the clinical course of SLE. The other patient who presented with pancytopenia was first diagnosed with HLH, and later with SLE. In her case, HLH turned out to be a presenting manifestation of SLE. We report on three successfully treated cases, and discuss the prevalence, characteristics, treatments, and prognosis of secondary HLH associated with SLE.
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등록된 정보가 없습니다.
참고문헌 (15)
참고문헌 신청
Kleynberg RL. / 2012 / Secondary hemophagocytic lymphohistiocytosis in adults : an update on diagnosis and therapy / Clin Adv Hematol Oncol 10:726~732
Lambotte O. / 2006 / Characteristics and long-term outcome of 15 episodes of systemic lupus erythematosusassociated hemophagocytic syndrome / Medicine(Baltimore) 85:169~182
Oh DH. / 1999 / A case of acute lupus hemophagocytic syndrome : a case report / J Korean Rheum Assoc 6:272~276
Parodi A. / 2009 / Macrophage activation syndrome in juvenile systemic lupus erythematosus : a multinational multicenter study of thirty-eight patients / Arthritis Rheum 60:3388~3399
Henter JI. / 2007 / HLH-2004 : diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis / Pediatr Blood Cancer 48:124~131
Lambotte O. / 2006 / Characteristics and long-term outcome of 15 episodes of systemic lupus erythematosusassociated hemophagocytic syndrome / Medicine(Baltimore) 85:169~182
Oh DH. / 1999 / A case of acute lupus hemophagocytic syndrome : a case report / J Korean Rheum Assoc 6:272~276
Parodi A. / 2009 / Macrophage activation syndrome in juvenile systemic lupus erythematosus : a multinational multicenter study of thirty-eight patients / Arthritis Rheum 60:3388~3399
Henter JI. / 2007 / HLH-2004 : diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis / Pediatr Blood Cancer 48:124~131
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